Tommaso D’Angelo, Alfredo Blandino, Michele B. Saitta, Salvatore Agati, Placido Romeo, Silvio Mazziotti
G. Martino University Hospital Messina. Bambino Gesù Children’s Hospital.
Italy
Annals of Thoracic Surgery
Ann Thorac Surg 2021; 112: e173-e176
DOI: 10.1016/j.athoracsur.2021.01.020
Abstract
Hypogenetic lung syndrome, also known as scimitar syndrome, is a rare and well-known congenital condition that includes hypoplastic right pulmonary artery and lung, right displacement of the heart, anomalous systemic arterial supply to the lung, and a characteristically curved anomalous right pulmonary vein draining into the inferior vena cava. In exceptional cases, the anomalous pulmonary vein may drain into left atrium. We here report a case of a 17-year-old girl with a rare variant of hypogenetic lung syndrome diagnosed by means of multimodality imaging and treated with percutaneous occlusion of the aortopulmonary collateral.
Category
Abnormal Systemic to Pulmonary Arterial Collaterals or Connections
Surgical and Catheter-mediated Interventions for Pulmonary Vascular Disease
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes