Janelle Buysse, Ramya Deepthi Billa, Daniel McLennan, Ravi Ashwath, Aditya Badheka, Madhuradhar Chegondi
University of Iowa Stead Family Children’s Hospital.
United States
Cureus
Cureus 2021; 13:
DOI: 10.7759/cureus.17203
Abstract
Infantile scimitar syndrome is associated with pulmonary hypertension which can be difficult to manage. We present a three-month-old infant with scimitar syndrome, who eventually developed refractory pulmonary hypertension, posing a significant management challenge. Further workup demonstrated contralateral pulmonary vein stenosis, which is rarely described in scimitar syndrome. Our index case highlights the importance of follow-up cardiac catheterizations in these patients with severe pulmonary hypertension.
Category
Class II. Pulmonary Hypertension Associated with Pulmonary Vein Stenosis
Age Focus: Pediatric Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes