Dicky Fakhri, Salomo Purba, Indriwanto Sakdijan, Ardiansyah, Aditya Agam Nugraha
National Cardiovascular Center Harapan Kita.
Indonesia
Journal of Cardiothoracic Surgery
J Cardiothorac Surg 2026;
DOI: 10.1186/s13019-026-04046-4
Abstract
Background: A late-presenting total anomalous pulmonary venous connection is extremely rare, and surgical repair remains a significant challenge.
Cases presentation: We present two cases of surgical repair for late-presenting supracardiac total anomalous pulmonary vein connection: a 14-year-old female and a 32-year-old female. Both were successfully operated on and were discharged on postoperative days 9 and 29. The second patient had a prolonged hospital stay due to complications of acute kidney injury after surgery and the need for hemodialysis. Both patients had a small left ventricle and pulmonary hypertension preoperatively. All pulmonary veins drained to a common pulmonary vein, which drained to a left-sided vertical vein, which drained into the innominate vein. Postoperative evaluation of both patients found no pulmonary vein obstruction and good biventricular contraction.
Conclusion: Late diagnosis may occur in TAPVC patients, but a surgical repair may still be possible.
Category
Class I. Pulmonary Hypertension Associated with Congenital Cardiovascular Disease
Age Focus: Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease
Fresh or Filed Publication: Fresh (PHresh). Less than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes