Sorachi Shimada, Tomomi Uyeda, Yoshichika Maeda, Takumi Kobayashi, Kanako Kishiki, Yuji Hamamichi, Satoshi Yazaki, Naoki Wada, Yukihiro Takahashi, In-Sam Park, Tadahiro Yoshikawa
Sakakibara Heart Institute. Asahikawa Medical University. Nishiogi Kimura Clinic.
Japan
Journal of Cardiology Cases
J Cardiol Cases 2022; 26: 345-347
DOI: 10.1016/j.jccase.2022.07.008
Abstract
Patients who have undergone an atrial switch operation for dextro-transposition of the great arteries (dTGA) sometimes suffer from right ventricular dysfunction, tricuspid regurgitation, arrhythmias, or baffle leaks. We report the first case of single-stage arterial switch operation conversion in an adult patient with dTGA and pulmonary arterial hypertension (PAH) due to a baffle leak after a Senning procedure. Perioperative mechanical circulatory support was required for 3 weeks. Although chronic kidney disease persisted, her left ventricular function and pulmonary hypertension improved over the first postoperative year. This is a rare case, and we believe that the patient’s PAH might have helped the left ventricle withstand systemic pumping for over two decades.
Category
Class I. Pulmonary Hypertension Associated with Congenital Heart Disease
Age Focus: Pediatric Pulmonary Vascular Disease or Adult Pulmonary Vascular Disease
Fresh or Filed Publication: Filed (PHiled). Greater than 1-2 years since publication
Article Access
Free PDF File or Full Text Article Available Through PubMed or DOI: Yes